par Vandeweyer, Eric ;De Saint Aubain, Nicolas ;Gebhart, Michaël
Référence Acta chirurgica Belgica (Ed. bilingue), 102, 6, page (455-458)
Publication Publié, 2002-12
Article révisé par les pairs
Résumé : Dermatofibrosarcoma protuberans is a rare mesenchimal tumour mainly characterized by its local aggressiveness and high reported recurrence rates. Classically, wide excisional surgery with at least 3 cm of free tissue margins is recommended as treatment. We present a series of 18 patients with variable gross free tissue margins but confirmed histological free margins in all cases whatever the surgical excision really was. Only one patient presented a local recurrence (5.5%) of a very large (14 cm) sarcomatous variant of dermatofibrosarcoma protuberans. Mean follow-up in this series was 52.1 months. Those results emphasize that histological rather than theoretical «golden rules» are mandatory to locally control this aggressive neoplasm.