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Torsade de pointes in Kearns-Sayre syndrome.

par Wilmin, Stéphan ;De Bels, David ;Knecht, Sébastien ;Gottignies, Philippe;Gazagnes, Marie-Dominique ;Devriendt, Jacques
Référence Practical neurology, 12, 3, page (199-201)
Publication Publié, 2012-06

Article révisé par les pairs

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Résumé :

A 47-year-old woman with Kearns-Sayre syndrome (KSS) and an implanted pacemaker for complete heart block was admitted to the intensive care unit following a cardiac arrest due to ventricular tachycardia (torsade de pointes) in the setting of QT prolongation. Complete heart blocks and ventricular tachycardia are implicated as mechanisms of sudden deaths in KSS; such patients may require pacemaker implantation and implantation of an automatic implantable cardioverter-defibrillator.