par Telerman Toppet, Nicole
;Khoubesserian, P.;Bacq, Michèle
;Durdu, Jacques
;Lambelin, Dominique
;Coërs, Christian 
Référence Muscle & nerve, 7, 6, page (439-441)
Publication Publié, 1984-08
;Khoubesserian, P.;Bacq, Michèle
;Durdu, Jacques
;Lambelin, Dominique
;Coërs, Christian 
Référence Muscle & nerve, 7, 6, page (439-441)
Publication Publié, 1984-08
Article révisé par les pairs
| Résumé : | A familial myopathy with predominantly proximal muscle atrophy is described. Although several clinical features such as sternomastoid and brachioradialis muscle involvement suggested Steinert disease, myotonia was not demonstrated by clinical examination or EMG. Histological data were consistent with myotonic dystrophy. |



