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An estimation of the incidence and demographic picture of the major hemoglobinopathies in Belgium (from a confidential inquiry).

par Gulbis, Béatrice ;Ferster, Alina ;Vermylen, C;Dresse, Marie-Françoise;Vanderfaeillie, Anna;Delannoy, André;Labarque, Veerle;Philippet, Pierre;Kentos, Alain ;Sztern, B;Deprijck, Bernard;Vertongen, Françoise ;Red Blood Cell Disorders Subcommittee of the Belgian Haematological Society,
Référence Hemoglobin, 32, 3, page (279-285)
Publication Publié, 2008

Article révisé par les pairs

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Résumé :

An estimation of the incidence and demographic picture of the major hemoglobinopathies in Belgium has been approached through a confidential inquiry sent to 228 pediatric and adult hematological departments. Forty-two percent of responses showed that 417 patients are known in Belgium: 83% with sickle cell disease, 13% with beta-thalassemia (beta-thal) major, 2% with beta-thal intermedia, and 1% with Hb H disease. Twenty-five percent of the sickle cell disease patients and 54% of those suffering from a beta-thal major were older than 20 years. Three hospitals ensure the follow-up of 70% of the patients and are situated in Brussels, Belgium; a follow-up of less than 20 patients was reported at 21 centers. These results confirm that sickle cell disease is the major hemoglobinopathy in Belgium; it concerns mostly pediatricians but adult hematologists are also confronted with these pathologies. Therefore, it is necessary to implement integrated programs of prevention and treatment.