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Mucoid impaction of the appendice revealing cystic fibrosis complicated by cirrhosis in a young adult without pulmonary lesions

par Glibert, André;Adler, Michael ;Engelholm, Louis ;Vanderelst, A.;Cremer, Michel
Référence Gastroentérologie clinique et biologique, 12, 5, page (493-496)
Publication Publié, 1988

Article révisé par les pairs

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Résumé :

A 22-year-old man presented with pain in the right iliac fossa. Clinical examination suggested appendicitis and showed splenomegaly. Echography and abdominal CT-sca suggested the diagnosis of cystic fibrosis based on the association of signs of cirrhosis and pancreatic atrophy. The sweat test was positive. The hypothesis of a mucoid appendicular impaction with spontaneous regression was retained based on clinical and radiological signs. This atypical presentation of cystic fibrosis underscores the frequency of obstructive intestinal which occasionally reveals the disease in the adult, and on the absence in this case of otherwise frequently associated problems such as signficant pulmonary disease and malnutrition.