Titre:
  • Eculizumab in anti-factor h antibodies associated with atypical hemolytic uremic syndrome.
Auteur:Diamante Chiodini, Benedetta; Davin, Jean-Claude; Corazza, Francis; Khaldi, Karim; Dahan, Karin; Ismaili, Khalid; Adams, Brigitte
Informations sur la publication:Pediatrics, 133, 6, page (e1764-e1768)
Statut de publication:Publié, 2014-06
Sujet CREF:Médecine pathologie humaine
Mots-clés:Anti-Factor H autoantibodies
Atypical hemolytic uremic syndrome
Cardiomyopathy
Eculizumab
Multisystemic aHUS
Neurologic involvement
Thrombotic microangiopathy
MeSH keywords:Antibodies, Monoclonal, Humanized -- adverse effects -- therapeutic use
Autoantibodies -- blood
Brain -- pathology
Brain Ischemia -- diagnosis -- drug therapy -- immunology
Child
Complement Factor H -- immunology
Creatinine -- blood
Dose-Response Relationship, Drug
Early Medical Intervention
Electrocardiography
Follow-Up Studies
Hemoglobinometry
Hemolytic-Uremic Syndrome -- diagnosis -- drug therapy -- immunology
Humans
Kidney Failure, Chronic -- diagnosis -- drug therapy -- immunology
Lactic Acid -- blood
Long-Term Care
Magnetic Resonance Imaging
Male
Myocardial Ischemia -- diagnosis -- drug therapy -- immunology
Recurrence -- prevention & control
Renal Dialysis
Note générale:Case Reports
Journal Article
SCOPUS: ar.j
Langue:Anglais
Identificateurs:urn:issn:0031-4005
info:doi/10.1542/peds.2013-1594
info:pii/peds.2013-1594
info:scp/84901823978
info:pmid/24843055