par Noterman, Jacques ;Massager, Nicolas ;Vloeberghs, Michael;Brotchi, Jacques
Référence Surgical neurology, 49, 3, page (302-305)
Publication Publié, 1998-03
Référence Surgical neurology, 49, 3, page (302-305)
Publication Publié, 1998-03
Article révisé par les pairs
Résumé : | BACKGROUND: Gardner's syndrome includes a clinical triad of familial polyposis coli, osteomas, and soft tissue tumors. METHODS: We present a very unusual case of probable isolated Gardner's syndrome characterized by extremely voluminous osteomas in the occipital and frontal areas associated with diffuse subcutaneous lipomas and without colic abnormality. RESULTS: The neurosurgical management included resection of the osteomas for cosmetic reasons. After a follow-up period of 5 years, the patient remains free of digestive complaints and the resected osteomas did not recur. CONCLUSIONS: The special clinical presentation of our case of possible Gardner's syndrome is discussed. |