par Ferster, Alina ;Capouet, Vincent ;Deville, Andrée;Fondu, Pierre ;Corazza, Francis
Référence Haemostasis, 23, 1, page (65-68)
Publication Publié, 1993
Référence Haemostasis, 23, 1, page (65-68)
Publication Publié, 1993
Article révisé par les pairs
Résumé : | We describe here successful open heart surgery with extracorporeal circulation and haemodilution in a child with severe congenital factor VII deficiency. Substitution therapy was realized with factor VII concentrate (SD proconvertin concentrate, Bio-Transfusion). This is the first report case of successful cardiac surgery in severe congenital factor VII deficiency. |