par Devière, Jacques ;Brohée, Dany ;Hiden, M.;Bourgeois, Nadine
Référence Journal of clinical gastroenterology, 10, 1, page (111-114)
Publication Publié, 1988
Article révisé par les pairs
Résumé : In a woman with hereditary hemorrhagic telangiectasia (HHT) (Osler-Weber-Rendu disease) who died of fulminant hepatitis B, autopsy revealed cirrhosis of the liver and diffuse hepatic telangiectasia. Her daughter and grandson also suffered from the hepatic involvement of HHT. Sufficient laboratory investigations were available to exclude known causes of cirrhosis. We review the relationship between Osler-Weber-Rendu disease and liver cirrhosis or fibrosis.