par Lubansu, Alphonse ;Rorive, Sandrine ;David, Philippe ;Sariban, Eric ;Seligmann, Roland;Brotchi, Jacques ;Pirotte, Benoît
Référence Child's nervous system, 20, 2, page (119-122)
Publication Publié, 2004-02
Référence Child's nervous system, 20, 2, page (119-122)
Publication Publié, 2004-02
Article révisé par les pairs
Résumé : | INTRODUCTION: Pleomorphic xanthoastrocytoma (PXA) is a rare brain glial tumour found in young patients. Most cases are reported as evolving low-grade neoplasms associated with a long survival after complete surgical resection. Some PXAs, however, can demonstrate secondary malignant transformation or progress with a short survival. Anaplastic histological features at first presentation or secondary meningeal dissemination have rarely been reported. CASE REPORT: We describe the case of a cerebral PXA in a 7-year-old girl presenting with anaplastic histological features and craniospinal meningeal dissemination that progressed rapidly with a poor outcome. |