Titre:
  • HDAC inhibitors correct frataxin deficiency in a Friedreich ataxia mouse model.
Auteur:Rai, Myriam; Soragni, Elisabetta; Jenssen, Kai; Burnett, Ryan; Herman, David; Coppola, Giovanni; Geschwind, Daniel H; Gottesfeld, Joel M; Pandolfo, Massimo
Informations sur la publication:PloS one, 3, 4, page (e1958)
Statut de publication:Publié, 2008
Sujet CREF:Sciences bio-médicales et agricoles
MeSH keywords:Acetylation -- drug effects
Animals
Cerebellum -- drug effects
Cerebellum -- metabolism
Chromatin -- metabolism
Disease Models, Animal
Enzyme Inhibitors -- pharmacology
Enzyme Inhibitors -- therapeutic use
Epigenesis, Genetic -- drug effects
Friedreich Ataxia -- drug therapy
Gene Expression Profiling
Histone Deacetylase Inhibitors
Histones -- metabolism
Introns -- genetics
Iron-Binding Proteins -- genetics
Iron-Binding Proteins -- metabolism
Mice
Myocardium -- metabolism
Protein Processing, Post-Translational -- drug effects
RNA, Messenger -- genetics
RNA, Messenger -- metabolism
Note générale:Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langue:Anglais
Identificateurs:urn:issn:1932-6203
info:doi/10.1371/journal.pone.0001958
info:scp/44349114629
info:pmid/18463734
PMC2373517