Titre:
  • Flanking domain stability modulates the aggregation kinetics of a polyglutamine disease protein.
Auteur:Saunders, Helen M; Gilis, Dimitri; Rooman, Marianne; Dehouck, Yves; Robertson, Amy L; Bottomley, Stephen P.
Informations sur la publication:Protein science, 20, 10, page (1675-1681)
Statut de publication:Publié, 2011-10
Sujet CREF:Biophysique
Biologie moléculaire
Mots-clés:Ataxin-3
Fibrillogenesis
Polyglutamine
Proten misfolding
MeSH keywords:Humans
Machado-Joseph Disease -- genetics -- metabolism
Models, Molecular
Mutation
Nerve Tissue Proteins -- chemistry -- genetics -- metabolism
Nuclear Proteins -- chemistry -- genetics -- metabolism
Peptides -- metabolism
Protein Folding
Protein Structure, Tertiary
Repressor Proteins -- chemistry -- genetics -- metabolism
Thermodynamics
Note générale:Journal Article
Research Support, Non-U.S. Gov't
FLWIN
SCOPUS: ar.j
Langue:Anglais
Identificateurs:urn:issn:0961-8368
info:doi/10.1002/pro.698
info:scp/80053156781
info:pmid/21780213
PMC3218360